MESENCHYMAL TUMOUR OR AMNIOTIC BAND SYNDROME IN A NEWBORN – A DIAGNOSTIC DILEMMA
Ivana Ježić, Sarah Bjedov, Anko Antabak, Krešimir Bulić
A suspicion of mesenchymal tumour of the right foot dorsum was raised in a newborn with amniotic band syndrome. A well defined spheric tumour occupied the entire foot dorsum, without edema of the rest of the foot distal to the constriction ring. An ultrasound scan defined the tumour as firm, localized and well vascularized, while the MR scan described the tissue as lymphedematous, although allowing other etiologies. CORE biopsy histology report did not reveal malignant cells, but still did not rule out mesenchymal tumour. A definite hystological analysis performed after tumour removal and Z-plasty confirmed the diagnosis of lymphedema. Correction of the constricting ring and tumour removal resulted in an excellent functional and aesthetic result. Such atypical lymphedema presentation resulting from amniotic constriction ring can raise suspicion of a solid mesenchymal tumor.